Atrofia coriorretiniana pigmentada paravenosa con afectación macular
- Romero Martín, Ricardo 2
- Castaño, A. 1
- Moriche-Carretero, Manuel 2
- Poyales Villamor, Blanca 2
- Granados, M. 2
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1
Hospital San Juan de Dios del Aljarafe
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Hospital San Juan de Dios del Aljarafe
Bormujos, España
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2
Hospital Universitario La Paz
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ISSN: 0365-6691
Year of publication: 2013
Volume: 88
Issue: 2
Pages: 77-79
Type: Article
More publications in: Archivos de la Sociedad Española de Oftalmologia
Abstract
Case report A 65-year-old female, with poor visual acuity in right eye since childhood, was referred to our hospital. Funduscopic examination revealed bone-spicule pigmentation and choroidal and retinal pigment epithelium atrophy along the vascular arcades, with macular involvement in right eye. The patient was diagnosed with pigmented paravenous retinochoroidal atrophy (PPRCA). Discussion PPRCA is a rare disease, of unknown origin, characterised by retinochoroidal atrophy and retinal pigmentation along retinal veins, generally without macular involvement. Latest publications show a slow progression. No effective treatment is available.