Atrofia coriorretiniana pigmentada paravenosa con afectación macular

  1. Romero Martín, Ricardo 2
  2. Castaño, A. 1
  3. Moriche-Carretero, Manuel 2
  4. Poyales Villamor, Blanca 2
  5. Granados, M. 2
  1. 1 Hospital San Juan de Dios del Aljarafe
    info

    Hospital San Juan de Dios del Aljarafe

    Bormujos, España

  2. 2 Hospital Universitario La Paz
    info

    Hospital Universitario La Paz

    Madrid, España

    ROR https://ror.org/01s1q0w69

Journal:
Archivos de la Sociedad Española de Oftalmologia

ISSN: 0365-6691

Year of publication: 2013

Volume: 88

Issue: 2

Pages: 77-79

Type: Article

DOI: 10.1016/J.OFTAL.2011.11.019 DIALNET GOOGLE SCHOLAR

More publications in: Archivos de la Sociedad Española de Oftalmologia

Abstract

Case report A 65-year-old female, with poor visual acuity in right eye since childhood, was referred to our hospital. Funduscopic examination revealed bone-spicule pigmentation and choroidal and retinal pigment epithelium atrophy along the vascular arcades, with macular involvement in right eye. The patient was diagnosed with pigmented paravenous retinochoroidal atrophy (PPRCA). Discussion PPRCA is a rare disease, of unknown origin, characterised by retinochoroidal atrophy and retinal pigmentation along retinal veins, generally without macular involvement. Latest publications show a slow progression. No effective treatment is available.