Enfermedades bullosas

  1. Pulido Pérez, A.
  2. Suárez Fernández, Ricardo
Journal:
Medicine: Programa de Formación Médica Continuada Acreditado

ISSN: 0304-5412

Year of publication: 2014

Issue Title: Enfermedades de la piel (I): dermatosis infecciosas, descamativas, bullosas y sistémicas

Series: 11

Issue: 47

Pages: 2774-2782

Type: Article

DOI: 10.1016/S0304-5412(14)70696-1 DIALNET GOOGLE SCHOLAR

More publications in: Medicine: Programa de Formación Médica Continuada Acreditado

Abstract

Bullous or bullous diseases represent a complex group of entities with common clinical features and different pathogenic mechanisms. Affecting the skin, mucous membranes and, occasionally, other epithelial tissues. Pemphigus and pemphigoid belong to the group of autoimmune bullous diseases. Despite its low incidence, have a high morbidity, so that knowledge of its main features is essential in clinical practice. Diagnosis should be made based on clinical findings, immunopathology and serology. Corticosteroids and immunosuppressive star in traditional therapeutic regimens. However, in recent years, new therapies have been developed which block the production of autoantibodies in these diseases and significantly decrease the side effects of chronic use of steroids and other immunosuppressive agents.

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